An eight year old healthy female child was referred for the management of raised intraocular pressure (IOP) in left eye. Examination of left eye revealed 3600 ectropion uveae, trabecular dysgenesis and glaucomatous disc. A diagnosis of congenital ectropion uveae with glaucoma was made. As IOP became refractory to maximal topical therapy, trabeculectomy with adjunctive Mitomycin-C had to be performed. The IOP normalized after surgery and is well maintained without any anti glaucoma medication. Early recognition of this rare anomaly and close monitoring of IOP is very crucial. Refractive nature of raised IOP needs to be promptly addressed at the earliest with trabeculectomy.
Wang GM, Thuente D, Bohnsack BL. Angle closure glaucoma in congenital ectropion uvea. Am J Ophthalmol Case Rep 2018;10:215-20.
Dowling JL Jr, Albert DM, Nelson LB, Walton DS. Primary glaucoma associated with iridotrabecular dysgenesis and ectropion uveae. Ophthalmol 1985;92(7):912-21.
Ritch R, Forbes M, Hetherington J Jr, Harrison R, Podos SM. Congenital ectropion uveae with glaucoma. Ophthalmol 1984;91(4):326-31.
Harasymowycz PJ, Papamatheakis DG, Eagle RC Jr, Wilson RP. Congenital ectropion uveae and glaucoma. Arch Ophthalmol 2006;124(2):271-3.
Wicherkiewicz B. Contribution to the knowledge of the ectropion uveae congenitum. Graefeβs Aech Ophthalmol 1891;37:204-7.
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How to Cite This Article
Vancouver
S K, R RN. Congenital unilateral ectropion uveae with refractory glaucoma [Internet]. Indian J Clin Exp Ophthalmol. 2019 [cited 2025 Oct 09];5(2):266-267. Available from: https://doi.org/10.18231/j.ijceo.2019.063
APA
S, K., R, R. N. (2019). Congenital unilateral ectropion uveae with refractory glaucoma. Indian J Clin Exp Ophthalmol, 5(2), 266-267. https://doi.org/10.18231/j.ijceo.2019.063
MLA
S, Kamala, R, Rashmi N. "Congenital unilateral ectropion uveae with refractory glaucoma." Indian J Clin Exp Ophthalmol, vol. 5, no. 2, 2019, pp. 266-267. https://doi.org/10.18231/j.ijceo.2019.063
Chicago
S, K., R, R. N.. "Congenital unilateral ectropion uveae with refractory glaucoma." Indian J Clin Exp Ophthalmol 5, no. 2 (2019): 266-267. https://doi.org/10.18231/j.ijceo.2019.063